A case report: Rapid progression of arrhythmogenic cardiomyopathy with biventricular failure
Mae-Sing Lim-Cooke 1 , Federico Fedel 1 , Mengfei Lu 1 * , Debashis Roy 1 2
More Detail
1 Princess Alexandra Hospital, Harlow, UK2 Department of Cardiology, Princess Alexandra Hospital, Harlow, UK* Corresponding Author

Abstract

Background: Arrhythmogenic cardiomyopathy (ACM) is an inherited condition. It is sub-characterized into arrhythmogenic right, left, and bi- ventricular cardiomyopathies. The Padua task force criteria is used in the diagnosis of ACM.
Case report: A 41-year-old presented with palpitations was found to be in ventricular tachycardia. He was reverted back into sinus rhythm following cardioversion. Electrocardiogram showed widespread T-wave inversions. Initial troponin was raised with unobstructed coronaries on coronary angiogram. Transthoracic echocardiogram (TTE) seven months prior showed reduced left ventricular systolic function (LVSD) with unremarkable right ventricular (RV) function. TTE on this admission showed new right sided failure with worsening LVSD. Cardiac magnetic resonance imaging (MRI) appearance was consistent with biventricular ACM based on morpho-functional criteria.
Discussion: This case highlights how RV function can decline rapidly in ACM. Widespread T-wave inversion is a minor criterion in the task force criteria. If TTE is indicative of underlying cardiomyopathy, cardiac MRI is the gold-standard investigation to confirm the pathology.

License

This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

ELECTRON J GEN MED, Volume 19, Issue 5, October 2022, Article No: em397

https://doi.org/10.29333/ejgm/12263

Publication date: 25 Jul 2022

Article Views: 881

Article Downloads: 870

Open Access References How to cite this article